Molecular Dx Significance 7/10

International Consensus Criteria Standardise T-PLL Diagnosis and Response Assessment

The T-PLL International Study Group published the first consensus guidelines for diagnosis, staging, treatment indication, and response assessment in T-cell prolymphocytic leukaemia. These standardised criteria are essential for enabling meaningful comparison across clinical trials and will support regulatory approval pathways for novel therapeutics in this rare T-cell malignancy.

The original study

Consensus criteria for diagnosis, staging, and treatment response assessment of T-cell prolymphocytic leukemia.

Authors
Staber PB, Herling M, Bellido M, Jacobsen ED, Davids MS, Kadia TM, et al.
Journal
Blood
Type
Journal Article, Review, Consensus Statement
PMID
31292114
Read the original study →

Original abstract

T-cell prolymphocytic leukemia (T-PLL) is a rare, mature T-cell neoplasm with a heterogeneous clinical course. With the advent of novel treatment options that will potentially change the management of patients with T-PLL, it has become necessary to produce consensus guidelines for the design and conduct of clinical trials. The T-PLL International Study group (TPLL-ISG) set out to define standardized criteria for diagnosis, treatment indication, and evaluation of response. These criteria will facilitate comparison of results from clinical trials in T-PLL, and will thus support clinical decision making, as well as the approval of new therapeutics by healthcare authorities.